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KMID : 0367419940370030422
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Journal of Korean Pediatric Society
1994 Volume.37 No. 3 p.422 ~ p.428
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A Case of Congenital Hypoprothrombinemia
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이종광
전혜원/이정화/이광철/김순겸
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Abstract
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Congenital hypoprothrombinemia is a rare congenital coagulation defect. The clinical signs are manifestation of generalized tendency such as; mucosal bleeding, hypermenorrhea and post tooth extraction hemorrage. It is associated with prolongation
of PT
and PTT with normal thrombin time and decreased serum prothrombin level.
A case with congenital hypoprothrombinemia was experienced by the authors. A 36 days old male baby was admitted with palor skin and vomiting started one day before admission. Right side brain parenchymal hemorrhage and left shift of lateral
ventricle
were on brain CT scan. Prologation of prothrombin time and partial prothrombin time with decreased serum prothrombin level were resulted. Serum factor I, V, VII, VIII, IX and X were within normal level.
We report a case congenital hypoprothrombinemia with a brief review of relaed literatures.
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